Case of the Week
Section Editors: Matylda Machnowska1 and Anvita Pauranik2
1University of Toronto, Toronto, Ontario, Canada
2BC Children's Hospital, University of British Columbia, Vancouver, British Columbia, Canada
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January 27, 2014
Solitary Extrapleural Fibrous Tumor
- Rare, usually benign tumor that originates from submesothelial, mesenchymal cells. Usually affects adults between 20-80 years of age, with no gender predilection.
- Sinonasal apperance is rare. When affecting nasal cavity, they present as painless, unilateral nasal fossa masses, with secondary nasal obstruction and epistaxis.
- Key Diagnostic Features: Well defined, expansile soft-tissue lesion on CT. Calcification or necrosis can sometimes be seen. On MRI studies, these lesions are isointense to muscle on T1WI and hypointense on T2WI. Heterogeneous enhancement is seen.
- DDx: Inflammatory polyp, papilloma, epithelial neoplasms, lymphoma, esthesioneuroblastoma, sarcoma
- Rx: Surgical resection