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Research ArticlePediatric Neuroimaging

Assessing Disease Severity in Late Infantile Neuronal Ceroid Lipofuscinosis Using Quantitative MR Diffusion-Weighted Imaging

J.P. Dyke, H.U. Voss, D. Sondhi, N.R. Hackett, S. Worgall, L.A. Heier, B.E. Kosofsky, A.M. Uluğ, D.C. Shungu, X. Mao, R.G. Crystal and D. Ballon
American Journal of Neuroradiology August 2007, 28 (7) 1232-1236; DOI: https://doi.org/10.3174/ajnr.A0551
J.P. Dyke
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H.U. Voss
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D. Sondhi
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N.R. Hackett
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S. Worgall
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L.A. Heier
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B.E. Kosofsky
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A.M. Uluğ
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D.C. Shungu
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X. Mao
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R.G. Crystal
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D. Ballon
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Article Information

vol. 28 no. 7 1232-1236
DOI 
https://doi.org/10.3174/ajnr.A0551
PubMed 
17698521

Published By 
American Journal of Neuroradiology
Print ISSN 
0195-6108
Online ISSN 
1936-959X
History 
  • Received October 10, 2006
  • Accepted after revision December 11, 2006
  • Published online August 13, 2007.

Copyright & Usage 
Copyright © American Society of Neuroradiology

Author Information

  1. J.P. Dykea,b,
  2. H.U. Vossa,b,
  3. D. Sondhic,
  4. N.R. Hackettc,
  5. S. Worgalld,
  6. L.A. Heierb,
  7. B.E. Kosofskyd,
  8. A.M. Uluğb,
  9. D.C. Shungua,b,
  10. X. Maoa,b,
  11. R.G. Crystalc and
  12. D. Ballona,b
  1. aCitigroup Biomedical Imaging Center, Weill Medical College of Cornell University, New York, NY
  2. bDepartment of Radiology, Weill Medical College of Cornell University, New York, NY
  3. cDepartment of Genetic Medicine, Weill Medical College of Cornell University, New York, NY
  4. dDepartment of Pediatrics, Weill Medical College of Cornell University, New York, NY
  1. Address correspondence to Jonathan P. Dyke, Citigroup Biomedical Imaging Center, Weill Cornell Medical College, Box 234, 1300 York Ave, New York, NY 10021; e-mail: jpd2001{at}med.cornell.edu
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J.P. Dyke, H.U. Voss, D. Sondhi, N.R. Hackett, S. Worgall, L.A. Heier, B.E. Kosofsky, A.M. Uluğ, D.C. Shungu, X. Mao, R.G. Crystal, D. Ballon
Assessing Disease Severity in Late Infantile Neuronal Ceroid Lipofuscinosis Using Quantitative MR Diffusion-Weighted Imaging
American Journal of Neuroradiology Aug 2007, 28 (7) 1232-1236; DOI: 10.3174/ajnr.A0551

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Assessing Disease Severity in Late Infantile Neuronal Ceroid Lipofuscinosis Using Quantitative MR Diffusion-Weighted Imaging
J.P. Dyke, H.U. Voss, D. Sondhi, N.R. Hackett, S. Worgall, L.A. Heier, B.E. Kosofsky, A.M. Uluğ, D.C. Shungu, X. Mao, R.G. Crystal, D. Ballon
American Journal of Neuroradiology Aug 2007, 28 (7) 1232-1236; DOI: 10.3174/ajnr.A0551
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Cited By...

  • Global and Widespread Local White Matter Abnormalities in Juvenile Neuronal Ceroid Lipofuscinosis
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  • Differential Diagnosis of Normal Pressure Hydrocephalus by MRI Mean Diffusivity Histogram Analysis
  • Assessment of Disease Severity in Late Infantile Neuronal Ceroid Lipofuscinosis Using Multiparametric MR Imaging
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  • Crossref (27)
  • Google Scholar

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  • Treatment of Late Infantile Neuronal Ceroid Lipofuscinosis by CNS Administration of a Serotype 2 Adeno-Associated Virus Expressing CLN2 cDNA
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    Molecular Genetics and Metabolism 2016 119 1-2
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  • Volumetric Description of Brain Atrophy in Neuronal Ceroid Lipofuscinosis 2: Supratentorial Gray Matter Shows Uniform Disease Progression
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    American Journal of Neuroradiology 2016 37 10
  • Prognostic Value of Quantitative Diffusion‐Weighted MRI in Patients with Traumatic Brain Injury
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