Article Figures & Data
Figures
- Fig 1.
A, Patient at 10 years old with a large, tumefactive, and hyperkeratotic epidermal nevus involving the skull, face, and neck. B, Note lines of Blaschko on the head and neck. Modified from Moss et al.4
- Fig 2.
MR angiography of the patient at 2 years old shows a hypoplastic right siphon and middle cerebral artery, with a stenotic Sylvian bifurcation.
- Fig 3.
A, Coronal T2-weighted image of the patient at 20 days old shows a right cerebral hemiatrophy with cortical thinning and mild parenchymal change in the temporal lobe (arrow). On the same side, macrocrania and dilated liquoral spaces are present. B, Coronal T2-weighted image of the patient at 2 years old shows hypomyelination and an old infarct (arrow) in the right temporal lobe. Next to the ventricle, confluent and enlarged VRSs are recognizable. C, MR image of the patient at 10 years old. Coronal T2-weighted image shows, on the right side, stable cerebral hemiatrophy, a giant VRS next to the ventricle, and old ischemic changes within the hypomyelinated temporal lobe. D, High-resolution axial T2-weighted image shows a scleroatrophic right eyeball with a hypoplastic optic nerve. Lipodermoid tissue in the lacrimal fossa is present (arrow).
