Article Figures & Data
Figures
- Fig 1.
A, Patient 1. Right carotid arteriography. Both cerebral hemispheres are supplied by the right internal carotid artery. Enlarged anterior cerebral artery (arrowhead). B, Same patient. Axial T2-weighted (200/100) image shows an abnormal small left hemisphere with a round gray matter mass (arrow), which is criss-crossed by several large vessels. C, Coronal MRA of the neck shows absence of the left internal carotid artery and hyperplasia of the right internal carotid artery (arrow). Normal size of both vertebral arteries (arrowheads).
- Fig 2.
Patient 3 at 16 years of age. A, Axial T1-weighted MR image shows hypoplasia of the left cerebral hemisphere with enlarged lateral ventricle and polymicrogyria in the same hemisphere. B, MRA study of the same patient. The axial view shows right internal carotid artery hyperplasia with vascularization of both anterior cerebral hemispheres from a large right anterior cerebral artery (large arrowhead) and poor vascularization of the left cerebral hemisphere. Collateral vascularization from the ophthalmic (arrow) and the external carotid arteries to the middle cerebral artery in the left side (small arrowhead).
- Fig 3.
A, Patient 5. Axial T1-weighted MR image shows hypoplasia of the left cerebral hemisphere with enlarged lateral ventricle and polymicrogyria of the anterior part of the hemisphere. B, Coronal view of MRA shows left carotid artery hyperplasia and intracavernous origin of the left anterior cerebral artery from which the right anterior cerebral artery (asterisk) also originates, and persistence of the trigeminal artery (arrow). The vertebrobasilar system is normal. C, Axial view of MRA shows the presence of the trigeminal artery in the left side (arrowhead).
Tables
Observed clinical, vascular, and cerebral abnormalities of 5 patients
Patient Age Sex Clinical Features MR Imaging MRA 1 11 y F Left frontal, palpebral, and nasal hemangioma Cortical dysplasia in the left hemisphere Left cerebral carotid aplasia. Right hemiparesis Seizures Left cerebral hemisphere hypoplasia Borderline ML 2 7 y F Left frontal, palpebral, and nasal hemangioma Left frontal polymicrogyria Persistence of left trigeminal and both proatlantal arteries Seizures Mild left cerebral hypoplasia Double kinking of the left internal carotid artery Borderline ML 3 16 y F Left frontal vascular malformation Left cerebral hemispheric polymicrogyria and hypoplasia Hypoplasia of the left internal carotid artery and the intracranial branches Seizures Right hemiparesis Borderline ML 4 6 mo F Left frontal and palpebral hemangioma Left cortical dysplasia Mild left cerebral hypoplasia Left carotid artery aplasia Dandy-Walker syndrome 5 3 y F Left frontal, orbital, and nasal hemangioma Left cerebral polymicrogyria-pachygyria Intracavernous origin of the left anterior cerebral artery Right hemiparesis Severe left cerebral hypoplasia Left persistent trigeminal artery Seizures Psychomotor delay Note:—F indicates female; ML, mental level.
