Article Figures & Data
Figures
- Fig 1
Patient 1, with lesion in left cerebral hemisphere.
A, Axial view fluid-attenuated inversion recovery image shows a very large cyst mass with thick nodular walls and mass effect but little edema.
B, T2-weighted fast spin-echo image, obtained at the same level, shows a necrotic mass with a thick heterogeneous wall causing midline shift.
C, Coronal view contrast-enhanced image shows a nodular rind of tumor. Remodeling of the calvarium by the mass can be seen (arrow).
D, CT bone window shows erosion of the left parietal bone (arrow) and faint calcification.
- Fig 2
Patient with left hemispheric mass.
A, Unenhanced CT scan displays a large doughnut-shaped mass with central cyst that opens into an eccentric large cystic component. Lesion has mass effect but little edema. Several calcifications are present in the tumor.
B, T2-weighted fast spin-echo image shows a large thick walled mass with mild surrounding edema. Note that the tumor is hypointense, presumably secondary to the calcifications.
C, Contrast-enhanced T1-weighted axial view image reveals a nodular peripheral enhancement in the thick calcified rind.
- Fig 3
Tectal mass. Mass with an eccentric cyst distorting the tectum can be seen.
- Fig 4
Cerebellopontile angle mass.
A, Fluid-attenuated inversion recovery image shows a right cerebellopontile angle extra-axial mass with solid and peripheral cystic components. Focal hypointensities correspond to calcifications shown on CT scans (not shown).
B, T2-weighted fast spin-echo image shows a right cerebellopontile angle extra-axial mass with solid and peripheral cystic components. Focal hypointensities correspond to calcifications shown on CT scans (not shown).
C, Contrast-enhanced image shows mild enhancement with a small, relatively more enhancing nodule.
Tables
Clinical, pathological, and imaging findings of four patients with the diagnosis of atypical teratoid/rhabdoid tumor
Patient No. Age/Sex Symptoms/Findings CT and MR Imaging Findings Resection Pathologic Findings Outcome Location/Invasion Composition Enhancement Calcification 1 9 mo/F R-sided weakness Cystic L frontoparietal occipital, skull destruction Solid and cystic, peripheral cyst Thick irregular nodular rim enhancement Yes GTR + Vimentin 7 mo no therapy other than surgery + GFAP + EMA + Cytokeratins − Synaptophysin − Actin 2 8 mo/F Poor feeding, macrocephaly, lethargy L hemisphere, infiltrative to adjacent parenchyma Solid and cystic Thick irregular nodular rim enhancement Yes STR + Vimentin 5 mo with therapy + GFAP + EMA 3 16 y/F R-sided weakness, numbness of the feet Tectal/pineal, brain stem invasion Solid and cystic, peripheral cyst Intense enhancement Yes STR + Vimentin 3 mo with therapy + GFAP + EMA − Synaptophysin − Actin − Ki-1 4 11 mo/M Multiple cranial nerve deficits Brain stem/R CPA, brain stem invasion Solid and cystic, peripheral cyst Moderate enhancement Yes STR + Vimentin 1 mo with therapy + GFAP + EMA + Cytokeratins Note.—F indicates Female; M, male; R, right; L, left; CPA, cerebellopontine angle; GTR, gross total resection; STR, subtotal resection; GFAP, glial fibrillary acidic protein; EMA, epithelial membrane antigen.
