Table 2:

Underlying diagnosis in our cohort of children with stroke and intracranial arterial stenosis (n = 41)

Clinical DiagnosisNo.
Moyamoya disease15
Neurofibromatosis type 1 with Moyamoya6
Trisomy-21 with Moyamoya3
Dissection2
Primary CNS vasculitis3
Varicella vasculitis2
TCA3
Sickle cell disease with Moyamoya3
Other
 Systemic large vessel vasculitis1
 Hemolytic uremic syndrome1
 Thalassemia with Moyamoya1
 Hurler syndrome1

  • Note:—TCA indicates transient cerebral arteriopathy.