Posterior fossa anomalies in 19 patients with PHACES with IAC enlargement

Age at Initial MRISexIAC EnhancingPosterior Petrous ProminenceCerebellar HypoplasiaOccipital BoneSide of Facial Hemangioma
3 moFYesaYesYesSmallerIpsilateral
1 moFYesaYesNoNoIpsilateral
2 moFYesaYesNoNoIpsilateral
4 moFYesaYesYesSmallerIpsilateral
38 dMYesNoYesLargerIpsilateral
9 moFYesYesYesSmallerIpsilateralb
29 moMYesYesYesSmallerIpsilateral
24 moFNoYesYesSmallerIpsilateral
18 moMNoYesYesSmallerIpsilateral
15 moFNoYesYesDeformedContralateral
4 moFNoYesYesSmallerIpsilateral
24 moFNoYesYesSmallerIpsilateral
21 dFNoYesYesLargerIpsilateral
32 dFNoYesYesLargerIpsilateral
18 yFNoYesYesSmallerIpsilateral
8 yFNANoYesSmallerIpsilateral
13 yFNAYesYesDeformedIpsilateral
17 yFNANoNoNoIpsilateral
8 dFNAYesYesLargerIpsilateral
  • Note:—NA indicates that the patient did not receive intravenous contrast.

  • a Enhancement involuted on subsequent study.

  • b Facial hemangioma was bilateral.