Table 2:

Differential diagnosis of SMART syndrome

Category and Differential Diagnosis
Neoplastic process:
 Tumor recurrence, leptomeningeal carcinomatosis
Ischemic or vascular process:
 Subacute brain infarction, cortical vein thrombosis, PRES
Infectious process:
 Cerebritis, meningoencephalitis
Hyperexcitability:
 Hemiplegic migraine, status epilepticus
Genetic disease (hyperexcitability):
 MELAS