RT Journal Article SR Electronic T1 Pulsatility Attenuation along the Carotid Siphon in Pseudoxanthoma Elasticum JF American Journal of Neuroradiology JO Am. J. Neuroradiol. FD American Society of Neuroradiology SP 2030 OP 2033 DO 10.3174/ajnr.A7288 VO 42 IS 11 A1 Bartstra, J.W. A1 van Tuijl, R.J. A1 de Jong, P.A. A1 Mali, W.P.T.M. A1 van der Schaaf, I.C. A1 Ruigrok, Y.M. A1 Rinkel, G.J.E. A1 Velthuis, B.K. A1 Spiering, W. A1 Zwanenburg, J.J.M. YR 2021 UL http://www.ajnr.org/content/42/11/2030.abstract AB SUMMARY: We compared velocity pulsatility, distensibility, and pulsatility attenuation along the intracranial ICA and MCA between 50 patients with pseudoxanthoma elasticum and 40 controls. Patients with pseudoxanthoma elasticum had higher pulsatility and lower distensibility at all measured locations, except for a similar distensibility at C4. The pulsatility attenuation over the siphon was similar between patients with pseudoxanthoma elasticum and controls. This finding suggests that other disease mechanisms are the main contributors to increased intracranial pulsatility in pseudoxanthoma elasticum.PIpulsatility indexPXEpseudoxanthoma elasticumSVDsmall-vessel disease2D-PC2D phase-contrast