RT Journal Article
SR Electronic
T1 MR Imaging of Dejerine-Sottas Disease
JF American Journal of Neuroradiology
JO Am. J. Neuroradiol.
FD American Society of Neuroradiology
SP 378
OP 380
VO 20
IS 3
A1 Maki, Daniel D.
A1 Yousem, David M.
A1 Corcoran, Celeste
A1 Galetta, Steven L.
YR 1999
UL http://www.ajnr.org/content/20/3/378.abstract
AB Summary: We report the MR findings in two patients with clinically and histologically proved Dejerine-Sottas disease. One patient had spinal involvement with multiple thickened and clumped nerve roots of the cauda equina; the second had multiple enlarged and enhancing cranial nerves. Although these findings are not specific for Dejerine-Sottas disease, they are suggestive of the diagnosis, which is further corroborated with history and confirmed with sural nerve biopsy and laboratory studies.